Surgical Treatment of Aortic Valve Papillary Fibroelastoma with Neurofibromatosis (von Recklinghausen’s Disease)

Yuki Okamoto, MD, Masahiko Matsumoto, MD, and Hidenori Inoue, MD

A 69-year-old man with a medical history of neurofibromatosis was transferred to our hospital for the treatment of an aortic valve mass. His workup identified an aortic valve papillary fibroelastoma based on the absence of signs of infection, thrombus in the left atrium, and valvular destruction or abnormal valvular function. A tumor was excised under cardiopulmonary bypass. The pathology of the mass was a papillary fibroelastoma. Neurofibromatosis with cardiac tumor is extremely rare. This is the first report of a case of papillary fibroelastoma associated with neurofibromatosis. (Ann Thorac Cardiovasc Surg 2010; 16: 213-215)

Key words: papillary fibroelastoma, neurofibromatosis

Second Department of Surgery, Faculty of Medicine, University of Yamanashi, Yamanashi, Japan

Received February 23, 2009; accepted for publication May 14, 2009
Address reprint requests to Yuki Okamoto, MD: Second Department of Surgery, Faculty of Medicine, University of Yamanashi, 1110 Shimokato, Chuo city, Yamanashi 409–3821, Japan.

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